Surgery for Congential Nasal Pyriform Aperture Stenosis (CNPAS)

Wood, John; Van Der Meer, Graeme

Surgery for Congential Nasal Pyriform Aperture Stenosis (CNPAS)

Open Education Resource

2025-03-31

Abstract

Congenital nasal pyriform aperture stenosis (CNPAS) is a very rare condition of the newborn, in which the nasal pyriform aperture is narrowed by bony overgrowth of the nasal process of the maxilla (Figure 1). As the narrowest point of the nasal airway, a small change in its diameter may significantly increase nasal airway resistance. As infants are obligate nose breathers for the first three months of life (or longer if premature), such an increased airway resistance causes functional airway obstruction and respiratory distress. While 1 in 5000 births has some form of congenital nasal airway obstruction, the majority is choanal atresia. The differential diagnosis includes nasal cavity masses, dacryocystocoeles, severe septal deviations and CNPAS.

Keywords

Surgery

Congential Nasal Pyriform Aperture Stenosis

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